On the heels of a news report about a 16 year-old boy in North Carolina who just died from a
, comes another report of a 38 year-old mom in Maine also diagnosed with a prion disease - soon-to-be fatal. Two different cases in
two different states, both in relatively young people.
What's happening? Reports about "Mad Cow" and other prion diseases started disappearing from the news after the media gagged Oprah back-when and then
vanished completely, following Bush's gag order on scientists
in 2005. Authorities
have been insisting that unlike Britain, we do not have the problem here. But now, it looks like the lid is off. Why? What else aren't they telling
I suspect the 16 year-old originally was infected via epigenetic inheritance, consider
infection unlikely, think a more rapidly progressive strain must be considered
- but most strongly suspect a super-imposed infection (probably flu) in both victims allowed already present prions to use the immune system to spread
in the body.
My ongoing concern about epidemics and pandemics is precisely that -
prions use the immune system to spread in the body
Given that infection with prions and other misfolded proteins is widespread, deaths are just the tip of the iceberg - the real problem is the burden
of chronic disease unleashed in survivors.
And this, I think, is why doctors suddenly are reporting prion-related deaths. We're about to see an uptick in prion-related deaths triggered by other
infections and as well, a huge surge in prion-related chronic disease.
NOTE: Protein misfolding can result in several different types of diseases
, including diseases that
are infectious, genetic, epigenetic, chronic, degenerative, and almost always debilitating. The list of "modern" diseases linked to prions,
prion-related proteins and other misfolded proteins is long, and still growing. Besides "Mad Cow Disease" or vCJD, this list includes cancers;
Alzheimer's and other dementias; diabetes; HIV/AIDS; Parkinson's; ALS; schizophrenia, depression, bipolar disorder, autism and other mental illnesses;
myositis; arthritis; stomache ailments like Crohn's and colitis; and many, many other chronic debilitating diseases. In short, virtually any organ or
body system can be affected, and few cases progress rapidly to encephalopathy
The New Patient: A young 38 year-old mom.
Another fast progression with no explanation; diagnosed as a prion disease within 3 months. Her symptoms started in November with a cough and vertigo.
Christmas Eve, stroke symptoms sent her to hospital, but doctors found no evidence of stroke. By mid-January, she had slurred speech, a loss of motor
skills, deteriorating vision, memory loss and was unable to walk. Days later she developed encephalitis (swelling of the brain).
Family hopes for miracle after young mom struck
After months of debilitating symptoms with no diagnosis, doctors this week say Sandi Tucker Kennedy, a 38-year-old wife and mom of four young children
ages 2 to 9, is believed to have a prion disease, a family of rare progressive neurodegenerative disorders that take over the neurological system.
“She's actually very young for it,” …
“The neurological condition is going to continue. It's a rapid-moving disease,” Tucker said. “The prognosis is four to 12 months from the onset
of symptoms and she's had symptoms for four months now.”
edit on 8/2/14 by soficrow because: format